oai:pubmedcentral.nih.gov:1018...
American Society of Neuroradiology
AJNR: American Journal of Neuroradiology
2023
25-03-2024
Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy.
Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry).
Recently, vessel wall MR imaging has shown increased sensitivity in the detection of subtle signs of parenchymal, leptomeningeal, and vestibulocochlear enhancement.
In this report, we describe a unique finding identified using this technique in a series of 6 patients with Susac syndrome and discuss its potential value for diagnostic work-up and follow-up.
Cardozo, P.,Marrodán, M.,Gilmore, A.,Fiol, M.P.,Chaves, H., 2023, Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome, American Society of Neuroradiology